252d5c88336cc2aaf0253525fec4395b pmc_10011476.pdf 8fa63d6e74aa6c11f7b46e1fa646b9e7713f0426 pmc_10011476.pdf 45d007fb5448253c53428f81e6669419250178e80c6e1c1f800c620b55784b54 pmc_10011476.pdf Title: Adjustment to disease and quality of life in people with vascular Ehlers-Danlos and Loeys-Dietz syndromes: A mixed-method study Subject: Background: Vascular Ehlers-Danlos (vEDS) and Loeys-Dietz syndromes (LDS) are hereditary disorders of connective tissue having severe vascular complications (HDCTv) which lead to an increased risk of premature death. Author: Carolina Baeza-Velasco; Nuria Rodriguez; Laura Parra; Teresa Gutiérrez-Rosado Creator: Adobe InDesign 14.0 (Windows) Producer: Adobe PDF Library 15.0 CreationDate: Tue Feb 21 08:10:06 2023 CET ModDate: Tue Feb 21 08:10:17 2023 CET Tagged: yes UserProperties: no Suspects: no Form: none JavaScript: no Pages: 10 Encrypted: no Page size: 595.276 x 841.89 pts (A4) Page rot: 0 File size: 418061 bytes Optimized: no PDF version: 1.6 name type encoding emb sub uni object ID ------------------------------------ ----------------- ---------------- --- --- --- --------- MBJAVF+MuseoSans-500 Type 1C Custom yes yes yes 8 0 KYKOTJ+MuseoSans-300 Type 1C Custom yes yes yes 1501 0 HWWWDP+MuseoSans-700 Type 1C Custom yes yes yes 55 0 GSHQPR+MuseoSans-300Italic Type 1C WinAnsi yes yes yes 1502 0 EPIENV+MinionPro-Regular Type 1C Custom yes yes yes 9 0 BIUMXB+MinionPro-It Type 1C Custom yes yes yes 10 0 YGGUHH+MuseoSans-500Italic Type 1C WinAnsi yes yes yes 75 0 XCWOTJ+MinionPro-BoldIt Type 1C WinAnsi yes yes yes 76 0 VZSCRN+STIXGeneral-Regular Type 1C WinAnsi yes yes yes 77 0 TWTLPR+MinionPro-Bold Type 1C WinAnsi yes yes yes 91 0 Jhove (Rel. 1.22.1, 2019-04-17) Date: 2023-05-25 02:25:43 CEST RepresentationInformation: pmc_10011476.pdf ReportingModule: PDF-hul, Rel. 1.12.1 (2019-04-17) LastModified: 2023-05-24 02:22:23 CEST Size: 418061 Format: PDF Version: 1.6 Status: Well-Formed and valid SignatureMatches: PDF-hul MIMEtype: application/pdf PDFMetadata: Objects: 1548 FreeObjects: 1 IncrementalUpdates: 0 DocumentCatalog: ViewerPreferences: HideToolbar: false HideMenubar: false HideWindowUI: false FitWindow: false CenterWindow: false DisplayDocTitle: false NonFullScreenPageMode: UseNone Direction: L2R ViewArea: CropBox ViewClip: CropBox PrintArea: CropBox PageClip: CropBox PageLayout: SinglePage PageMode: UseNone Language: en-GB Outlines: Item: Title: Adjustment to disease and quality of life in people with vascular Ehlers-Danlos and Loeys-Dietz syndromes: A mixed-method study Children: Item: Title: Introduction Item: Title: Method Children: Item: Title: Design and participants Item: Title: Instruments Item: Title: Procedure Item: Title: Analyses Item: Title: Results Children: Item: Title: Quantitative results Item: Title: Comparison between HDCTv and HS Item: Title: Comparison between HDCTv and hEDS Item: Title: Qualitative results Item: Title: Discussion Item: Title: Data availability statement Item: Title: Ethics statement Item: Title: Author contributions Item: Title: Conflict of interest Item: Title: Publisher’s note Item: Title: References Info: Title: Adjustment to disease and quality of life in people with vascular Ehlers-Danlos and Loeys-Dietz syndromes: A mixed-method study Author: Carolina Baeza-Velasco; Nuria Rodriguez; Laura Parra; Teresa Gutiérrez-Rosado Subject: Background: Vascular Ehlers-Danlos (vEDS) and Loeys-Dietz syndromes (LDS) are hereditary disorders of connective tissue having severe vascular complications (HDCTv) which lead to an increased risk of premature death. 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