A 28-year old white female with best-corrected visual acuity of 20/200 in both eyes, nystagmus, and characteristic anomaloscope findings for an achromat was tested. She complained of impaired visual acuity, poor color vision, and photoaversion, which had not changed over the years. Fundus exam was normal with the exception of a blunted foveal reflex in each eye. Photopic ERG responses were nondetectable while scotopic responses were within normal limits.