Results overview: Found 4 records in 0.03 seconds.
Articles, 4 records found
Articles 4 records found  
1.
10 p, 3.8 MB Machine Learning Improves Risk Stratification in Myelodysplastic Neoplasms : An Analysis of the Spanish Group of Myelodysplastic Syndromes / Mosquera Orgueira, Adrian (Complexo Hospitalario Universitario de Santiago de Compostela. Department of Hematology) ; Perez Encinas, Manuel Mateo (Complexo Hospitalario Universitario de Santiago de Compostela. Department of Hematology) ; Diaz Varela, Nicolas (Hospital Universitario Central de Asturias) ; Mora, Elvira (Hematology Department. Hospital Universitario y Politécnico la Fe) ; Díaz-Beyá, Marina (Hospital Clínic i Provincial de Barcelona) ; Montoro, María Julia (Vall d'Hebron Institut d'Oncologia) ; Pomares, Helena (Hematology Department. Hospital Duran i Reynals) ; Ramos, Fernando (Department of Hematology. Hospital Universitario de León) ; Tormo, Mar (Hospital Clínic Universitari (València)) ; Jerez, Andres (Hematology and Medical Oncology Department. Hospital Morales Meseguer) ; Nomdedeu, Josep F. (Institut d'Investigació Biomèdica Sant Pau) ; De Miguel Sanchez, Carlos (Arabako Unibertsitate Ospitalea (Vitoria, País Basc)) ; Leonor, Arenillas (Institut Hospital del Mar d'Investigacions Mèdiques) ; Cárcel, Paula (Department of Hematology. Hospital Público Universitario de la Ribera) ; Cedena Romero, María Teresa (Hospital 12 de Octubre (Madrid)) ; Xicoy, Blanca (Institut Germans Trias i Pujol. Institut de Recerca contra la Leucèmia Josep Carreras) ; Rivero, Eugenia (Department of Hematology. University Hospital Arnau de Vilanova) ; Del Orbe Barreto, Rafael Andres (Hospital Universitario Cruces Servicio de Hematología) ; Diez-Campelo, María (Hospital Universitario de Salamanca) ; Benlloch, Luis E. (Grupo Español de Síndromes Mielodisplásicos) ; Crucitti, Davide (Instituto de Investigacions Sanitarias de Santiago de Compostela) ; Valcárcel, David (Vall d'Hebron Institut d'Oncologia)
Myelodysplastic neoplasms (MDS) are a heterogeneous group of hematological stem cell disorders characterized by dysplasia, cytopenias, and increased risk of acute leukemia. As prognosis differs widely between patients, and treatment options vary from observation to allogeneic stem cell transplantation, accurate and precise disease risk prognostication is critical for decision making. [...]
2023 - 10.1097/HS9.0000000000000961
HemaSphere, Vol. 7 Núm. 10 (november 2023) , p. E961  
2.
8 p, 187.8 KB Real-world analysis of main clinical outcomes in patients with polycythemia vera treated with ruxolitinib or best available therapy after developing resistance/intolerance to hydroxyurea / Álvarez Larrán, Alberto (Institut d'Investigacions Biomèdiques August Pi i Sunyer) ; Garrote, Marta (Institut d'Investigacions Biomèdiques August Pi i Sunyer) ; Ferrer-Marín, Francisca (Universidad Católica San Antonio de Murcia) ; Pérez-Encinas, Manuel (Hospital Clínico Universitario) ; Mata-Vazquez, M.Isabel (Hospital Costa del Sol (Marbella)) ; Bellosillo Paricio, Beatriz (Hospital del Mar (Barcelona, Catalunya)) ; Arellano-Rodrigo, Eduardo (Institut d'Investigacions Biomèdiques August Pi i Sunyer) ; Gómez, Montse (Hospital Clínico) ; García, Regina (Hospital Universitario Virgen de la Victoria (Màlaga, Andalusia)) ; Garcia-Gutierrez, Valentin (Instituto Ramón y Cajal de Investigación Sanitaria (Madrid)) ; Gasior, Mercedes (Hospital Universitario La Paz (Madrid)) ; Cuevas, Beatriz (Hospital Universitario de Burgos) ; Angona, Anna (Hospital Universitari de Girona Doctor Josep Trueta) ; Gómez-Casares, María Teresa (Hospital Universitario de Gran Canaria Dr. Negrín) ; Martínez, Clara (Institut d'Investigació Biomèdica Sant Pau) ; Magro, Elena (Hospital Príncipe de Asturias) ; Ayala, Rosa (Hospital Universitario 12 de Octubre (Madrid)) ; Del Orbe Barreto, Rafael Andrés (Hospital Universitario de Cruces (Barakaldo, País Basc)) ; Pérez-López, Raúl (Hospital Universitario Virgen de la Arrixaca (Múrcia)) ; Fox, Maria Laura (Hospital Universitari Vall d'Hebron) ; Raya, José-Maria (Hospital Universitario de Canarias (La Laguna)) ; Guerrero, Lucía (Hospital Río Carrión) ; García-Hernández, Carmen (Hospital General) ; Caballero, Gonzalo (Hospital Universitario Miguel Servet (Saragossa)) ; Murillo, Ilda (Hospital San Jorge) ; Xicoy, Blanca (Institut Germans Trias i Pujol. Institut de Recerca contra la Leucèmia Josep Carreras) ; Ramírez, M.José (Hospital General) ; Carreño-Tarragona, Gonzalo (Hospital Universitario 12 de Octubre (Madrid)) ; Hernandez-Boluda, Juan Carlos (Hospital Clínico) ; Pereira, Aarturo (Institut d'Investigacions Biomèdiques August Pi i Sunyer)
Background: Ruxolitinib is approved for patients with polycythemia vera (PV) who are resistant/intolerant to hydroxyurea, but its impact on preventing thrombosis or disease-progression is unknown. Methods: A retrospective, real-world analysis was performed on the outcomes of 377 patients with resistance/intolerance to hydroxyurea from the Spanish Registry of Polycythemia Vera according to subsequent treatment with ruxolitinib (n = 105) or the best available therapy (BAT; n = 272). [...]
2022 - 10.1002/cncr.34195
Cancer, Vol. 128 Núm. 13 (january 2022) , p. 2441-2448  
3.
9 p, 1.4 MB Usefulness of NGS for Diagnosis of Dominant Beta-Thalassemia and Unstable Hemoglobinopathies in Five Clinical Cases / Rizzuto, Valeria (Universitat de Barcelona. Departament de Medicina) ; Koopmann, Tamara T. (Leiden University Medical Center) ; Blanco, Adoración (Hospital Universitari Vall d'Hebron) ; Tazón-Vega, Bárbara (Hospital Universitari Vall d'Hebron) ; Idrizovic, Amira (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Díaz de Heredia, Cristina (Hospital Universitari Vall d'Hebron) ; Del Orbe Barreto, Rafael Andrés (Hospital Universitario de Cruces (Barakaldo, País Basc)) ; Pampliega, Miriam Vara (Hospital Universitario de Cruces (Barakaldo, País Basc)) ; Velasco, Pablo (Hospital Universitari Vall d'Hebron) ; Beneitez Pastor, David (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Santen, Gijs Santen W.E. (Leiden University Medical Center) ; Waisfisz, Quinten (VU Medical Center) ; Elting, Mariet (VU Medical Center) ; Smiers, Frans J.W. (Leiden University Medical Center) ; de Pagter, Anne J. (Leiden University Medical Center) ; Kerkhoffs, Jean Louis H. (AGA City Hospital) ; Harteveld, Cornelis L. (Leiden University Medical Center) ; Mañú Pereira, María del Mar (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Institut Germans Trias i Pujol. Institut de Recerca contra la Leucèmia Josep Carreras
Unstable hemoglobinopathies (UHs) are rare anemia disorders (RADs) characterized by abnormal hemoglobin (Hb) variants with decreased stability. UHs are therefore easily precipitating, causing hemolysis and, in some cases, leading to dominant beta-thalassemia (dBTHAL). [...]
2021 - 10.3389/fphys.2021.628236
Frontiers in physiology, Vol. 12 (may 2021) , p. 628236  
4.
12 p, 926.4 KB Combined study of 13 and complement genes in the diagnosis of thrombotic microangiopathies using next-generation sequencing / Fidalgo, Teresa (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Martinho, Patrícia (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Pinto, Catarina S. (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Oliveira, Ana C. (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Salvado, Ramon (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Borràs, Nina (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Coucelo, Margarida (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Manco, Licínio (University of Coimbra) ; Maia, Tabita (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Mendes, M. João (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Del Orbe Barreto, Rafael Andrés (Instituto de Investigación Sanitaria Biocruces Bizkaia) ; Corrales Insa, Irene (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Vidal, Francisco (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Ribeiro, M. Letícia (Centro Hospitalar e Universitário de Coimbra (Coimbra, Portugal)) ; Universitat Autònoma de Barcelona
The 2 main forms of thrombotic microangiopathy () are thrombotic thrombocytopenic purpura () and atypical hemolytic uremic syndrome (). Deficiency of 13 and dysregulation of the complement pathway result in and , respectively; however, overlap of their clinical characteristics makes differential diagnosis challenging. [...]
2017 - 10.1002/rth2.12016
Research and Practice in Thrombosis and Haemostasis, Vol. 1 (june 2017) , p. 69-80  

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