Resultats globals: 3 registres trobats en 0.03 segons.
Articles, 3 registres trobats
Articles 3 registres trobats  
1.
16 p, 6.7 MB Mutations in HID1 Cause Syndromic Infantile Encephalopathy and Hypopituitarism / Schänzer, Anne (Institute of Neuropathology, Justus-Liebig-University, Giessen, Germany) ; Achleitner, Melanie T. (University Children's Hospital, Paracelsus Medical University (PMU), Salzburg, Austria) ; Trümbach, Dietrich (Institute of Metabolism and Cell Death, Helmholtz Center, Munich, Germany) ; Hubert, Laurence (Inserm UMR1163, Imagine Institute, Tanslational Genetics, Université de Paris, Paris, France) ; Munnich, Arnold (Inserm UMR1163, Imagine Institute, Tanslational Genetics, Université de Paris, Paris, France) ; Ahlemeyer, Barbara (Institute for Anatomy and Cell Biology, Division of Medical Cell Biology, Justus Liebig University, Giessen, Germany) ; AlAbdulrahim, Maha M. (King Abdullah Bin Abdulaziz University Hospital, Riyadh, Saudi Arabia) ; Greif, Philipp A. (Experimental Leukemia and Lymphoma Research Department of Medicine III, University Hospital, LMU Munich, Munich, Germany) ; Vosberg, Sebastian (German Cancer Research Centre (DKFZ), Heidelberg, Germany) ; Hummer, Blake (Molecular and Cellular Biophysics Program, Department of Biological Sciences, University of Denver, Denver, CO, USA) ; Feichtinger, René G. (University Children's Hospital, Paracelsus Medical University (PMU), Salzburg, Austria) ; Mayr, Johannes A. (University Children's Hospital, Paracelsus Medical University (PMU), Salzburg, Austria) ; Wortmann, Saskia B. (Radboud Center for Mitochondrial Medicine, Department of Pediatrics, Amalia Children's Hospital, Radboudumc, Nijmegen, The Netherlands) ; Aichner, Heidi (Department of Pediatrics, Academic Teaching Hospital, Landeskrankenhaus Feldkirch, Feldkirch, Austria) ; Rudnik-Schöneborn, Sabine (Division of Human Genetics, Medical University of Innsbruck, Innsbruck, Austria) ; Ruiz, Anna (Parc Taulí Hospital Universitari. Institut d'Investigació i Innovació Parc Taulí (I3PT)) ; Gabau, Elisabeth (Parc Taulí Hospital Universitari. Institut d'Investigació i Innovació Parc Taulí (I3PT)) ; Pérez Sánchez, Jacobo (Parc Taulí Hospital Universitari. Institut d'Investigació i Innovació Parc Taulí (I3PT)) ; Ellard, Sian (College of Medicine and Health, University of Exeter, Exeter, UK) ; Homfray, Tessa (Saint George's University Hospital and Royal Brompton Hospital, London, UK) ; Stals, Karen L. (Genomic Laboratory, Royal Devon & Exeter NHS Foundation Trust, Exeter, UK) ; Wurst, Wolfgang (Ludwig-Maximilians-Universität München) ; Neubauer, Bernd A. (Department of Child Neurology, Justus-Liebig-University, Giessen, Germany) ; Acker, Till (Institute of Neuropathology, Justus-Liebig-University, Giessen, Germany) ; Bohlander, Stefan K. (Leukaemia and Blood Cancer Research Unit, Department of Molecular Medicine and Pathology, The University of Auckland, Auckland, New Zealand) ; Asensio, Cédric (Molecular and Cellular Biophysics Program, Department of Biological Sciences, University of Denver, Denver, CO, USA) ; Besmond, Claude (Inserm UMR1163, Imagine Institute, Tanslational Genetics, Université de Paris, Paris, France) ; Alkuraya, Fowzan S. (Department of Translational Genomics, Center for Genomic Medicine, King Faisal Specialist Hospital and Research Center, Riyadh, Saudi Arabia) ; AlSayed, Moenaldeen D. (King Faisal Specialist Hospital and Research Centre (Aràbia Saudita)) ; Hahn, Andreas (Department of Child Neurology, Justus-Liebig-University, Giessen, Germany) ; Weber, Axel (Institute of Human Genetics, Justus-Liebig- University, Giessen, Germany) ; Universitat Autònoma de Barcelona
Precursors of peptide hormones undergo posttranslational modifications within the trans-Golgi network (TGN). Dysfunction of proteins involved at different steps of this process cause several complex syndromes affecting the central nervous system (CNS). [...]
2021 - 10.1002/ana.26127
Annals of neurology, Vol. 90 (june 2021) , p. 143-158  
2.
6 p, 1.5 MB Following the steps of a reaction by direct imaging of many individual molecules / Van Vörden, Dennis (University of Duisburg-Essen. Center for Nanointegration Duisburg-Essen) ; Wortmann, Ben (University of Duisburg-Essen. Center for Nanointegration Duisburg-Essen) ; Schmidt, Nico (University of Duisburg-Essen. Center for Nanointegration Duisburg-Essen) ; Lange, Manfred (University of Duisburg-Essen. Center for Nanointegration Duisburg-Essen) ; Robles, Roberto (Institut Català de Nanociència i Nanotecnologia) ; Brendel, Lothar (University of Duisburg-Essen. Center for Nanointegration Duisburg-Essen) ; Bobisch, Christian A. (University of Duisburg-Essen. Center for Nanointegration Duisburg-Essen) ; Möller, Rolf (University of Duisburg-Essen. Center for Nanointegration Duisburg-Essen)
The dehydrogenation and dechlorination of FeOEP-Cl on Cu(111) has been studied in detail by scanning tunneling microscopy. Although, it is not possible to follow the reaction of an individual molecule, the complete pathway of the reaction with 22 inequivalent intermediate states and the rates of the involved processes are revealed. [...]
2016 - 10.1039/c6cc02959k
Chemical communications, Vol. 52, Issue 49 (June 2016) , p. 7711-7714  
3.
18 p, 3.2 MB Reversible 2D Phase Transition Driven by an Electric Field : Visualization and Control on the Atomic Scale / Wortmann, Ben (University of Duisburg-Essen. Faculty of Physics. Center for Nanointegration Duisburg-Essen (CENIDE)) ; Vörden, D. V. (University of Duisburg-Essen. Faculty of Physics. Center for Nanointegration Duisburg-Essen (CENIDE)) ; Graf, P. (University of Duisburg-Essen. Faculty of Physics. Center for Nanointegration Duisburg-Essen (CENIDE)) ; Robles, Roberto (Institut Català de Nanociència i Nanotecnologia) ; Abufager, Paula (Institut Català de Nanociència i Nanotecnologia) ; Lorente Palacios, Nicolás (Institut Català de Nanociència i Nanotecnologia) ; Bobisch, Christian A (University of Duisburg-Essen. Faculty of Physics. Center for Nanointegration Duisburg-Essen (CENIDE)) ; Möller, Rolf (University of Duisburg-Essen. Faculty of Physics. Center for Nanointegration Duisburg-Essen (CENIDE))
We report on a reversible structural phase transition of a two-dimensional system that can be locally induced by an external electric field. Two different structural configurations may coexist within a CO monolayer on Cu(111). [...]
2016 - 10.1021/acs.nanolett.5b04174
Nano letters, Vol. 16, Núm. 1 (January 2016) , p. 528-533  

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2 Wortmann, Ben
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