Dipòsit Digital de Documents de la UAB 4 registres trobats  La cerca s'ha fet en 0.01 segons. 
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11 p, 4.3 MB Combined intramuscular and intraspinal transplant of bone marrow cells improves neuromuscular function in the SOD1 G93A mice / Martínez Muriana, Anna (Centro de Investigación Biomédica en Red sobre Enfermedades Neurodegenerativas) ; Pastor, Diego (UMH-CSIC. Instituto de Neurociencias) ; Mancuso, Renzo (KU Leuven. VIB Center for Brain and Disease Research) ; Rando, Amaya (Universidad de Zaragoza. Laboratorio de Genética Bioquímica) ; Osta, Rosario (Universidad de Zaragoza. Laboratorio de Genética Bioquímica) ; Martínez, Salvador (UMH-CSIC. Instituto de Neurociencias) ; López Vales, Rubèn (Centro de Investigación Biomédica en Red sobre Enfermedades Neurodegenerativas) ; Navarro, X. (Xavier) (Xavier) (Universitat Autònoma de Barcelona. Facultat de Medicina)
The simultaneous contribution of several etiopathogenic disturbances makes amyotrophic lateral sclerosis (ALS) a fatal and challenging disease. Here, we studied two different cell therapy protocols to protect both central and peripheral nervous system in a murine model of ALS. [...]
2020 - 10.1186/s13287-020-1573-6
Stem cell research & therapy, Vol. 11 (february 2020)  
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16 p, 1.8 MB Chemotherapeutic agent 5-fluorouracil increases survival of SOD1 mouse model of ALS / Rando, Amaya (Instituto de Investigación Sanitaria Aragón. Centro de Investigación Biomédica de Aragón (CIBA)) ; De La Torre, M. (Instituto de Investigación Sanitaria Aragón. Centro de Investigación Biomédica de Aragón (CIBA)) ; Martínez-Muriana, Anna (Universitat Autònoma de Barcelona. Institut de Neurociències) ; Zaragoza, Pilar (Instituto de Investigación Sanitaria Aragón. Centro de Investigación Biomédica de Aragón (CIBA)) ; Musaro, A. (Center for Life Nano Science@Sapienza. Istituto Italiano di Tecnologia) ; Hernández Estañol, Sara (Institut de Recerca Biomèdica de Lleida) ; Navarro, X. (Xavier) (Xavier) (Universitat Autònoma de Barcelona. Institut de Neurociències) ; Toivonen, J. M. (Instituto de Investigación Sanitaria Aragón. Centro de Investigación Biomédica de Aragón (CIBA)) ; Osta, R. (Instituto de Investigación Sanitaria Aragón. Centro de Investigación Biomédica de Aragón (CIBA))
Amyotrophic lateral sclerosis (ALS) is a lethal motor neuron disease with no cure. Currently there are only two ALS drugs approved by the FDA, both with a limited therapeutic effect. In the search for drug candidates for ALS, we studied the effect of known stem cell mobilizing agents (treatment) and antimetabolite 5-fluorouracil (5-FU) (anti-treatment) in SOD1G93A model of ALS. [...]
2019 - 10.1371/journal.pone.0210752
PloS one, Vol. 14 Núm. 1 (january 2019) , p. e0210752  
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12 p, 3.2 MB Intramuscular transplantation of bone marrow cells prolongs the lifespan of SOD1 G93A mice and modulates expression of prognosis biomarkers of the disease / Rando, Amaya (Zaragoza, Spain) ; Pastor, Diego (Alicante, Spain) ; Viso-León, Mari Carmen (Alicante, Spain) ; Martínez, Anna (Universitat Autònoma de Barcelona. Departament de Biologia Cel·lular, de Fisiologia i d'Immunologia) ; Manzano Martínez, Raquel (Universidad de Zaragoza) ; Navarro, X. (Xavier) (Xavier) (Universitat Autònoma de Barcelona. Departament de Biologia Cel·lular, de Fisiologia i d'Immunologia) ; Osta, Rosario (Zaragoza, Spain) ; Martínez, Salvador (Alicante, Spain)
Amyotrophic lateral sclerosis (ALS) is a neurodegenerative disorder characterized by progressive muscle weakness, paralysis and death. There is no effective treatment for ALS and stem cell therapy has arisen as a potential therapeutic approach. [...]
2018 - 10.1186/s13287-018-0843-z
Stem cell research & therapy, Vol. 9 (april 2018)  
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10 p, 3.4 MB Neuroprotective Effect of Non-viral Gene Therapy Treatment Based on Tetanus Toxin C-fragment in a Severe Mouse Model of Spinal Muscular Atrophy / Oliván, Sara (Centro de Investigación Biomédica en Red de Bioingeniería, Biomateriales y Nanomedicina) ; Calvo, Ana Cristina (Universidad de Zaragoza. Facultad de Veterinaria. Laboratorio de Genética Bioquímica) ; Rando, Amaya (Universidad de Zaragoza. Facultad de Veterinaria. Laboratorio de Genética Bioquímica) ; Herrando-Grabulosa, Mireia (Universitat Autònoma de Barcelona. Institut de Neurociències) ; Manzano Martínez, Raquel (University of Oxford. Department of Physiology, Anatomy and Genetics) ; Zaragoza, Pilar (Universidad de Zaragoza. Instituto Agroalimentario de Aragón) ; Tizzano, Eduardo F. (Hospital Universitari Vall d'Hebron) ; Aguilera, José (Universitat Autònoma de Barcelona. Institut de Neurociències) ; Osta, Rosario (Centro de Investigación y Tecnología Agroalimentaria de Aragón) ; Universitat Autònoma de Barcelona. Departament de Bioquímica i de Biologia Molecular
Spinal muscular atrophy (SMA) is a hereditary childhood disease that causes paralysis and progressive degeneration of skeletal muscles and spinal motor neurons. SMA is associated with reduced levels of full-length Survival of Motor Neuron (SMN) protein, due to mutations in the Survival of Motor Neuron 1 gene. [...]
2016 - 10.3389/fnmol.2016.00076
Frontiers in molecular neuroscience, Vol. 9 (August 2016) , art. 76  

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