UAB Digital Repository of Documents 7 records found  Search took 0.01 seconds. 
1.
13 p, 1.6 MB Refining Kidney Survival in 383 Genetically Characterized Patients With Nephronophthisis / König, Jens Christian (Department of General Pediatrics, University Children's Hospital Münster) ; Karsay, Rebeka (Department of General Pediatrics, University Children's Hospital Münster) ; Gerß, Joachim (Institute of Biostatistics and Clinical Research, University of Münster) ; Schlingmann, Karl-Peter (Department of General Pediatrics, University Children's Hospital Münster) ; Dahmer-Heath, Mareike (Department of General Pediatrics, University Children's Hospital Münster) ; Telgmann, Anna-Katharina (Department of General Pediatrics, University Children's Hospital Münster) ; Kollmann, Sabine (Department of General Pediatrics, University Children's Hospital Münster) ; Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ; Gillion, Valentine (Division of Nephrology, Saint-Luc Academic Hospital, Université Catholique Louvain) ; Bockenhauer, Detlef (Great Ormond Street Hospital for Children (Londres)) ; Bertholet-Thomas, Aurélia (Centre de Référence des Maladies Rénales Rares-Néphrogones-Hôpital Femme Mère Enfant, Hospices Civils de Lyon-Filière ORKiD) ; Mastrangelo, Antonio (Fondazione Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Ca' Granda Ospedale Maggiore Policlinico) ; Boyer, Olivia (Hôpital Necker-Enfants Malades, Université de Paris) ; Lilien, Marc (Department of Pediatric Nephrology, University Medical Center Utrecht) ; Decramer, Stéphane (Université Toulouse III Paul-Sabatier) ; Schanstra, Joost. P. (Université Toulouse III Paul-Sabatier) ; Pohl, Martin (Department of Pediatrics, University Hospital Freiburg) ; Schild, Raphael (University Medical Center Hamburg-Eppendorf) ; Weber, Stefanie (University Children's Hospital) ; Hoefele, Julia (Institut für Humangenetik) ; Drube, Jens (Departement of Pediatric Nephrology, Medical School Hannover) ; Cetiner, Metin (Department of Pediatric Nephrology, University of Duisburg-Essen) ; Hansen, Matthias (Clementine Kinderhospital) ; Thumfart, Julia (Charité - Universitätsmedizin Berlin) ; Tönshoff, Burkhard (Department of Pediatrics I, University Children's Hospital Heidelberg) ; Habbig, Sandra (Department of Pediatric, University of Cologne) ; Liebau, Max Christoph (University Hospital Cologne and Medical) ; Bald, Martin (Children's Hospital (Alemanya)) ; Bergmann, Carsten (Medizinische Genetik Mainz (Alemanya)) ; Pennekamp, Petra (Department of General Pediatrics, University Children's Hospital Münster) ; Konrad, Martin (Department of General Pediatrics, University Children's Hospital Münster) ; Universitat Autònoma de Barcelona
Nephronophthisis (NPH) comprises a group of rare disorders accounting for up to 10% of end-stage kidney disease (ESKD) in children. Prediction of kidney prognosis poses a major challenge. We assessed differences in kidney survival, impact of variant type, and the association of clinical characteristics with declining kidney function. [...]
2022 - 10.1016/j.ekir.2022.05.035
Kidney International Reports, Vol. 7 (june 2022) , p. 2016-2028  
2.
11 p, 703.6 KB Use and Safety of Remdesivir in Kidney Transplant Recipients With COVID-19 / Buxeda, Anna (Institut Hospital del Mar d'Investigacions Mèdiques) ; Arias Cabrales, Carlos E (Institut Hospital del Mar d'Investigacions Mèdiques) ; Pérez-Sáez, María josé (Institut Hospital del Mar d'Investigacions Mèdiques) ; Cacho, Judit (Institut Germans Trias i Pujol. Hospital Universitari Germans Trias i Pujol) ; Cabello Pelegrin, Sheila (Hospital Universitari Son Espases (Palma de Mallorca, Balears)) ; Melilli, Edoardo (Hospital Universitari de Bellvitge) ; Aladrén, María José (Hospital Universitario Miguel Servet (Saragossa)) ; Galeano Alvarez, Cristina (Instituto Ramón y Cajal de Investigación Sanitaria (Madrid)) ; Lorenzo, Iinmaculada (Complejo Hospitalario Universitario de Albacete) ; Mazuecos, Auxiliadora (Hospital Universitario Puerta del Mar (Cadis, Andalusia)) ; Saura, Isabel María (Hospital Universitario Virgen de la Arrixaca (Múrcia)) ; Franco, Antonio (Hospital General Universitario de Alicante (Alacant, País Valencià)) ; Ruiz-Fuentes, María del Carmen. (Hospital Universitario Virgen de las Nieves (Granada)) ; Sánchez-Cámara, Luis Alberto (Hospital General Universitario Gregorio Marañón. Instituto de Investigación Sanitaria Gregorio Marañón (IiSGM)) ; Siverio, Orlando (Hospital Universitario Nuestra Señora de Candelaria (Santa Cruz de Tenerife)) ; Martin, María Luisa (Hospital Arnau de Vilanova (Lleida, Catalunya)) ; González-García, Elena (Hospital Universitario La Paz (Madrid)) ; López, Verónica (Instituto de Investigación Biomédica de Málaga) ; Martin-Moreno, Paloma Leticia (Instituto de Investigación Sanitaria de Navarra) ; Moina, Iñigo (Hospital de Basurto (Bilbao, Biscaia)) ; Moral Berrio, Esperanza (Hospital General Universitario de Ciudad Real) ; Moreso, Francesc (Hospital Universitari Vall d'Hebron) ; Portolés, José María (Hospital Universitario Puerta de Hierro Majadahonda (Madrid)) ; Santana-Estupiñán, Raquel (Hospital Universitario de Gran Canaria Dr. Negrín) ; Zárraga, Sofía (Hospital Universitario de Cruces (Barakaldo, País Basc)) ; Canal Girol, Cristina (Institut d'Investigació Biomèdica Sant Pau) ; Sánchez-Álvarez, Emilio (Hospital Universitario de Cabueñes (Gijón)) ; Pascual, Julio (Pascual Santos) (Institut Hospital del Mar d'Investigacions Mèdiques) ; Crespo, Marta (Institut Hospital del Mar d'Investigacions Mèdiques)
Introduction: Remdesivir has demonstrated antiviral activity against coronavirus, shortening the time to recovery in adults hospitalized with moderate/severe COVID-19. Severe adverse events such as acute kidney injury have been reported. [...]
2021 - 10.1016/j.ekir.2021.06.023
Kidney International Reports, Vol. 6 Núm. 9 (september 2021) , p. 2305-2315  
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2 p, 302.4 KB Transjugular Kidney Biopsy as a Safe Method to Increase the Etiological Diagnosis in Kidney Disease / Bolufer Cardona, Mónica (Hospital Universitari Vall d'Hebron) ; Soler, María José (Hospital Universitari Vall d'Hebron) ; McMahon, Gearoid M. (Harvard Medical School. Department of Medicine) ; Universitat Autònoma de Barcelona
2021 - 10.1016/j.ekir.2021.08.007
Kidney International Reports, Vol. 6 Núm. 10 (october 2021) , p. 2535-2536  
4.
11 p, 1.4 MB Hepatic Lactate Dehydrogenase A : An RNA Interference Target for the Treatment of All Known Types of Primary Hyperoxaluria / Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ; Barrios, Kelly (Dicerna Pharmaceuticals, Inc., Lexington) ; Brown, Bob D. (Dicerna Pharmaceuticals, Inc., Lexington) ; Hoppe, Bernd (German Hyperoxaluria Center Cologne/Bonn) ; Rosskamp, Ralf (Dicerna Pharmaceuticals, Inc., Lexington) ; Langman, Craig B. (Ann and Robert H. Lurie Children's Hospital of Chicago) ; Universitat Autònoma de Barcelona
Primary hyperoxaluria (PH) is a family of 3 rare genetic disorders of hepatic glyoxylate metabolism that lead to overproduction and increased renal excretion of oxalate resulting in progressive renal damage. [...]
2021 - 10.1016/j.ekir.2021.01.029
Kidney International Reports, Vol. 6 (february 2021) , p. 1088-1098  
5.
5 p, 1.6 MB Effects of SNF472, a Novel Inhibitor of Hydroxyapatite Crystallization in Patients Receiving Hemodialysis - Subgroup Analyses of the CALIPSO Trial / Raggi, Paolo (Division of Cardiology and Department of Medicine, University of Alberta, Edmonton, Alberta, Canada) ; Bellasi, Antonio (Research, Innovation and Brand Reputation Unit, ASST Papa Giovanni XXIII, Bergamo, Italy) ; Sinha, Smeeta (Department of Renal Medicine, Salford Royal NHS Foundation Trust, Salford, United Kingdom) ; Bover, Jordi (Institut d'Investigació Biomèdica Sant Pau) ; Rodriguez, Mariano (Hospital Universitario Reina Sofía (Còrdova, Espanya)) ; Ketteler, Markus (Department of General Internal Medicine and Nephrology, Robert-Bosch-Krankenhaus, Stuttgart, Germany) ; Bushinsky, David A. (Department of Medicine, University of Rochester School of Medicine, Rochester, New York, USA) ; Garg, Rekha (PharmaDRS, LLC, San Diego, California, USA) ; Perelló, Joan (University of the Balearic Islands, Palma, Spain) ; Gold, Alex (Department of Medicine, Stanford University, Palo Alto, California, USA) ; Chertow, Glenn M. (Department of Medicine, Stanford University, Palo Alto, California, USA) ; Universitat Autònoma de Barcelona
Coronary artery calcium (CAC) is highly prevalent and linked with poor outcomes in patients receiving maintenance hemodialysis, and its reduction may improve patient prognosis. SNF472, a selective inhibitor of hydroxyapatite crystallization, slows CAC progression in patients receiving maintenance hemodialysis. [...]
2020 - 10.1016/j.ekir.2020.09.032
Kidney International Reports, Vol. 5 (november 2020) , p. 2178-2182  
6.
3 p, 133.9 KB Feasible Low-Phosphorus Dietary Patterns in Maintenance Hemodialysis Patients : Need for Original Research / Bover, Jordi (Institut d'Investigació Biomèdica Sant Pau) ; Molina, Pablo (Hospital Universitari Doctor Peset (València)) ; Ureña-Torres, Pablo (Department of Renal Physiology, Necker Hospital, University of Paris Descartes, Paris, France) ; Arenas Jimenez, Maria Dolores (Institut Hospital del Mar d'Investigacions Mèdiques) ; Universitat Autònoma de Barcelona
2020 - 10.1016/j.ekir.2020.09.008
Kidney International Reports, Vol. 5 (september 2020) , p. 1845-1847  
7.
12 p, 571.6 KB Randomized Controlled Trial Assessing the Impact of Tacrolimus Versus Cyclosporine on the Incidence of Posttransplant Diabetes Mellitus / Torres, Armando (Hospital Universitario de Canarias (La Laguna)) ; Hernández, Domingo (Instituto de Investigación Biomédica de Málaga) ; Moreso, Francesc (Universitat Autònoma de Barcelona. Departament de Medicina) ; Seron, Daniel (Universitat Autònoma de Barcelona. Departament de Medicina) ; Burgos, María Dolores (Instituto de Investigación Biomédica de Málaga) ; Pallardó, Luis M. (Hospital Universitari Doctor Peset (València)) ; Kanter, Julia (Hospital Universitari Doctor Peset (València)) ; Díaz Corte, Carmen (Hospital Universitario Central de Asturias) ; Rodríguez, Minerva (Hospital Universitario Central de Asturias) ; Díaz Gómez, Juan Manuel (Institut d'Investigació Biomèdica Sant Pau) ; Silva, Irene (Institut d'Investigació Biomèdica Sant Pau) ; Valdes, Francisco (Complejo Hospitalario Universitario de A Coruña) ; Fernández-Rivera, Constantino (Complejo Hospitalario Universitario de A Coruña) ; Osuna, Antonio (Hospital Universitario Virgen de las Nieves (Granada)) ; Gracia Guindo, María C. (Hospital Universitario Virgen de las Nieves (Granada)) ; Gómez Alamillo, Carlos (Hospital Universitario Marqués de Valdecilla (Santander, Cantabria)) ; Ruiz, Juan C. (Hospital Universitario Marqués de Valdecilla (Santander, Cantabria)) ; Marrero Miranda, Domingo (Hospital Universitario de Canarias (La Laguna)) ; Pérez-Tamajón, Lourdes (Hospital Universitario de Canarias (La Laguna)) ; Rodríguez, Aurelio (Hospital Universitario de Canarias (La Laguna)) ; González-Rinne, Ana (Hospital Universitario de Canarias (La Laguna)) ; Alvarez, Alejandra (Hospital Universitario de Canarias (La Laguna)) ; Perez-Carreño, Estefanía (Hospital Universitario de Canarias (La Laguna)) ; de la Vega Prieto, María José (Hospital Universitario de Canarias (La Laguna)) ; Henriquez, Fernando (Hospital Universitario de Gran Canaria Dr. Negrín) ; Gallego Samper, Roberto (Hospital Universitario de Gran Canaria Dr. Negrín) ; Salido, Eduardo (Hospital Universitario de Canarias (La Laguna)) ; Porrini, Esteban (Hospital Universitario de Canarias (La Laguna)) ; Universitat Autònoma de Barcelona
Despite the high incidence of posttransplant diabetes mellitus (PTDM) among high-risk recipients, no studies have investigated its prevention by immunosuppression optimization. We conducted an open-label, multicenter, randomized trial testing whether a tacrolimus-based immunosuppression and rapid steroid withdrawal (SW) within 1 week (Tac-SW) or cyclosporine A (CsA) with steroid minimization (SM) (CsA-SM), decreased the incidence of PTDM compared with tacrolimus with SM (Tac-SM). [...]
2018 - 10.1016/j.ekir.2018.07.009
Kidney International Reports, Vol. 3 (july 2018) , p. 1304-1315  

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