|
1.
|
|
47 p, 14.4 MB |
Festival de primavera 1985
/
Donizetti, Gaetano ;
Chausson, Carlos ;
Coviello, Roberto ;
Gandolfi, Romano ;
Ghazarian, Sona ;
Kraus, Alfredo ;
Martín Regueiro, Maria Antonia ;
Salesky, Brian ;
Weikl, Bernd ;
Wixell, Ingvar ;
Cor del Gran Teatre del Liceu ;
Orquestra del Gran Teatre del Liceu ;
Societat del Gran Teatre del Liceu
1985 (Temporada de primavera 1985)
|
|
|
2.
|
|
|
3.
|
|
|
4.
|
|
14 p, 3.9 MB |
Low survival rate and muscle fiber-dependent aging effects in the McArdle disease mouse model
/
Real-Martinez, A. (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Brull, A. (Sorbonne Université. INSERM UMRS_974. Center of Research in Myology) ;
Huerta, J. (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Tarrasó, G. (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Lucia, A. (Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER)) ;
Martin, M.A. (Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER)) ;
Arenas, J. (Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER)) ;
Andreu, A.L. (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Nogales Gadea, Gisela (Institut Germans Trias i Pujol) ;
Vissing, J. (Copenhagen Neuromuscular Center. Department of Neurology. Rigshospitalet. University of Copenhagen) ;
Krag, Thomas (Copenhagen Neuromuscular Center. Department of Neurology. Rigshospitalet. University of Copenhagen) ;
de Luna, N. (Institut d'Investigació Biomèdica Sant Pau) ;
Pinós, T. (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Universitat Autònoma de Barcelona
McArdle disease is an autosomal recessive disorder caused by the absence of the muscle glycogen phosphorylase, which leads to impairment of glycogen breakdown. The McArdle mouse, a model heavily affected by glycogen accumulation and exercise intolerance, was used to characterize disease progression at three different ages. [...]
2019 -  10.1038/s41598-019-41414-8
Scientific reports (Nature Publishing Group), Vol. 9 Núm. 1 (january 2019) , p. 5116
|
|
|
5.
|
|
|
6.
|
|
|
7.
|
|
|
8.
|
|
|
9.
|
|
17.3 KB |
Sodium valproate increases the brain isoform of glycogen phosphorylase : looking for a compensation mechanism in McArdle disease using a mouse primary skeletal-muscle culture in vitro
/
de Luna, Noemí (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Brull, Astrid (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Guiu, Josep Maria (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Lucia, Alejandro (Instituto de Investigación 'i+12') ;
Martin, Miguel Angel (Instituto de Investigación 'i+12') ;
Arenas, Joaquin (Instituto de Investigación 'i+12') ;
Martí Seves, Ramon (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Andreu, Antoni L. (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Pinós, Tomàs (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Universitat Autònoma de Barcelona
McArdle disease, also termed 'glycogen storage disease type V', is a disorder of skeletal muscle carbohydrate metabolism caused by inherited deficiency of the muscle-specific isoform of glycogen phosphorylase (GP-MM). [...]
2015 - 10.1242/dmm.020230
Disease Models & Mechanisms, Vol. 8 (may 2015) , p. 467-472
|
|
|
10.
|
|
4 p, 163.0 KB |
McArdle disease does not affect skeletal muscle fibre type profiles in humans
/
Kohn, Tertius Abraham (UCT/MRC Research Unit for Exercise Science and Sports Medicine, Department of Human Biology, University of Cape Town) ;
Noakes, Timothy David (UCT/MRC Research Unit for Exercise Science and Sports Medicine, Department of Human Biology, University of Cape Town) ;
Rae, Dale Elizabeth (UCT/MRC Research Unit for Exercise Science and Sports Medicine, Department of Human Biology, University of Cape Town) ;
Rubio, Juan Carlos (Mitochondrial and Neuromuscular Diseases Laboratory, i+12 Research Institute, Hospital 12 de Octubre) ;
Santalla, Alfredo (Department of Sport Science, Universidad Pablo de Olavide) ;
Nogales Gadea, Gisela (Institut d'Investigació Biomèdica Sant Pau) ;
Pinós, Tomas (Hospital Universitari Vall d'Hebron. Institut de Recerca ) ;
Martín, Miguel A. (Mitochondrial and Neuromuscular Diseases Laboratory, i+12 Research Institute, Hospital 12 de Octubre) ;
Arenas, Joaquin (Mitochondrial and Neuromuscular Diseases Laboratory, i+12 Research Institute, Hospital 12 de Octubre) ;
Lucia, Alejandro (European University of Madrid) ;
Universitat Autònoma de Barcelona
Patients suffering from glycogen storage disease V (McArdle disease) were shown to have higher surface electrical activity in their skeletal muscles when exercising at the same intensity as their healthy counterparts, indicating more muscle fibre recruitment. [...]
2014 - 10.1242/bio.20149548
Biology open, Vol. 3 (november 2014) , p. 1224-1227
|
|
guest ::
email alert
or subscribe to the 
RSS feed.
