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10 p, 851.6 KB |
Recomendaciones de manejo de la afectación renal en el complejo esclerosis tuberosa
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Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Buj Pradilla, María José (Hospital 12 de Octubre (Madrid)) ;
Furlano, Monica (Institut d'Investigació Biomèdica Sant Pau) ;
Martínez, V. (Hospital Universitario Virgen de la Arrixaca (Múrcia)) ;
Matamala, Anna (Institut d'Investigació Biomèdica Sant Pau) ;
Morales, M. (Hospital 12 de Octubre (Madrid)) ;
Robles, N.R. (Hospital Universitario de Badajoz.) ;
Sans, Laia (Hospital del Mar (Barcelona, Catalunya)) ;
Villacampa, F. (Clínica Universidad de Navarra) ;
Torra Balcells, Roser (Institut d'Investigació Biomèdica Sant Pau) ;
Universitat Autònoma de Barcelona
El complejo esclerosis tuberosa (CET) es una enfermedad rara, hereditaria, multisistémica y con un amplio espectro fenotípico. Su manejo requiere de la colaboración de múltiples especialistas. Así como en la edad pediátrica cobra un especial relieve el neurólogo pediatra, en la edad adulta la afectación renal es la causante de la mayor morbimortalidad. [...]
2020 -  10.1016/j.nefroe.2020.03.009
Nefrología (Badalona. English), Vol. 40 Núm. 2 (marzo 2020) , p. 142-151
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10 p, 676.5 KB |
Expert guidance on the multidisciplinary management of cystinosis in adolescent and adult patients
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Levtchenko, Elena (Department of Pediatrics, University Hospitals Leuven Campus Gasthuisberg (Bélgica)) ;
Servais, Aude (Nephrology and Transplantation Department, Hôpital Necker Enfants Malades APHP (França)) ;
Hulton, Sally A (Department of Nephrology, Birmingham Women's and Children's Hospital NHS Foundation Trust (Regne Unit)) ;
Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Emma, Francesco (Ospedale Pediatrico Bambino Gesù-IRCCS (Itàlia)) ;
Game, David S (Department of Renal Medicine, Guy's and St Thomas' NHS Foundation Trust (Regne Unit)) ;
Lange, Karin (Hannover Medical School (Alemanya)) ;
Lapatto, Risto (Department of Pediatrics, Children's Hospital, Helsinki University Hospital and University of Helsinki) ;
Liang, Hong (CHNO des Quinze-Vingts, IHU ForeSight (França)) ;
Sberro-Soussan, Rebecca (Paris Descartes University-Sorbonne Paris Cité) ;
Topaloglu, Rezan (Hacettepe University (Turquia)) ;
Das, Anibh M (Clinic for Paediatric Kidney-, Liver- and Metabolic Diseases (Alemanya)) ;
Webb, Nicholas J A (Department of Paediatric Nephrology, University of Manchester) ;
Wanner, Christoph (University Hospital Würzburg (Alemanya)) ;
Universitat Autònoma de Barcelona
Cystinosis, a rare autosomal recessive lysosomal storage disorder, results in an abnormal accumulation of the amino acid cystine in multiple organs and tissues of the body. Renal symptoms typically develop in the first few months of life, with extra-renal manifestations becoming apparent over the next 10-20 years, which require coordinated multidisciplinary care. [...]
2022 - 10.1093/ckj/sfac099
Clinical Kidney Journal, Vol. 15 (april 2022) , p. 1675-1684
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13 p, 587.1 KB |
Post-authorisation safety study of burosumab use in paediatric, adolescent and adult patients with X-linked hypophosphataemia : rationale and description
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Brandi, Maria Luisa (FIRMO Foundation (Itàlia)) ;
Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Beck-Nielsen, Signe (Aarhus University Hospital (Aarhus, Dinamarca)) ;
Boot, Annemieke (University of Groningen) ;
Briot, Karine (Université de Paris) ;
de Lucas-Collantes, Carmen (Universidad Autónoma de Madrid) ;
Emma, Francesco (Bambino Gesù Children's Hospital IRCCS (Itàlia)) ;
Giannini, Sandro (University of Padua) ;
Haffner, Dieter (Children's Hospital (Alemanya)) ;
Keen, Richard (Royal National Orthopaedic Hospital NHS Trust (Regne Unit)) ;
Levtchenko, Elena (University Hospitals Leuven) ;
Mӓkitie, Outi (Helsinki University Hospital) ;
Nilsson, Ola (Karolinska Institutet and University Hospital) ;
Schnabel, Dirk (Charitè, University Medicine) ;
Tripto-Shkolnik, Liana (Tel-Aviv University) ;
Zillikens, M. Carola (Department of Internal Medicine, Erasmus MC Bone Center - Erasmus University Medical Center, Rotterdam (Holanda)) ;
Liu, Jonathan (Kyowa Kirin International (Regne Unit)) ;
Tudor, Alina (Kyowa Kirin International (Regne Unit)) ;
Mughal, M. Zulf (Royal Manchester Children's Hospital) ;
Universitat Autònoma de Barcelona
X-linked hypophosphataemia (XLH) is a rare, inherited, phosphate-wasting disorder that elevates fibroblast growth factor 23 (FGF23), causing renal phosphate-wasting and impaired active vitamin D (1,25(OH)D) synthesis. [...]
2022 - 10.1177/20406223221117471
Therapeutic Advances in Chronic Disease, Vol. 13 (september 2022)
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13 p, 1.6 MB |
Refining Kidney Survival in 383 Genetically Characterized Patients With Nephronophthisis
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König, Jens Christian (Department of General Pediatrics, University Children's Hospital Münster) ;
Karsay, Rebeka (Department of General Pediatrics, University Children's Hospital Münster) ;
Gerß, Joachim (Institute of Biostatistics and Clinical Research, University of Münster) ;
Schlingmann, Karl-Peter (Department of General Pediatrics, University Children's Hospital Münster) ;
Dahmer-Heath, Mareike (Department of General Pediatrics, University Children's Hospital Münster) ;
Telgmann, Anna-Katharina (Department of General Pediatrics, University Children's Hospital Münster) ;
Kollmann, Sabine (Department of General Pediatrics, University Children's Hospital Münster) ;
Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Gillion, Valentine (Division of Nephrology, Saint-Luc Academic Hospital, Université Catholique Louvain) ;
Bockenhauer, Detlef (Great Ormond Street Hospital for Children (Londres)) ;
Bertholet-Thomas, Aurélia (Centre de Référence des Maladies Rénales Rares-Néphrogones-Hôpital Femme Mère Enfant, Hospices Civils de Lyon-Filière ORKiD) ;
Mastrangelo, Antonio (Fondazione Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Ca' Granda Ospedale Maggiore Policlinico) ;
Boyer, Olivia (Hôpital Necker-Enfants Malades, Université de Paris) ;
Lilien, Marc (Department of Pediatric Nephrology, University Medical Center Utrecht) ;
Decramer, Stéphane (Université Toulouse III Paul-Sabatier) ;
Schanstra, Joost. P. (Université Toulouse III Paul-Sabatier) ;
Pohl, Martin (Department of Pediatrics, University Hospital Freiburg) ;
Schild, Raphael (University Medical Center Hamburg-Eppendorf) ;
Weber, Stefanie (University Children's Hospital) ;
Hoefele, Julia (Institut für Humangenetik) ;
Drube, Jens (Departement of Pediatric Nephrology, Medical School Hannover) ;
Cetiner, Metin (Department of Pediatric Nephrology, University of Duisburg-Essen) ;
Hansen, Matthias (Clementine Kinderhospital) ;
Thumfart, Julia (Charité - Universitätsmedizin Berlin) ;
Tönshoff, Burkhard (Department of Pediatrics I, University Children's Hospital Heidelberg) ;
Habbig, Sandra (Department of Pediatric, University of Cologne) ;
Liebau, Max Christoph (University Hospital Cologne and Medical) ;
Bald, Martin (Children's Hospital (Alemanya)) ;
Bergmann, Carsten (Medizinische Genetik Mainz (Alemanya)) ;
Pennekamp, Petra (Department of General Pediatrics, University Children's Hospital Münster) ;
Konrad, Martin (Department of General Pediatrics, University Children's Hospital Münster) ;
Universitat Autònoma de Barcelona
Nephronophthisis (NPH) comprises a group of rare disorders accounting for up to 10% of end-stage kidney disease (ESKD) in children. Prediction of kidney prognosis poses a major challenge. We assessed differences in kidney survival, impact of variant type, and the association of clinical characteristics with declining kidney function. [...]
2022 - 10.1016/j.ekir.2022.05.035
Kidney International Reports, Vol. 7 (june 2022) , p. 2016-2028
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14 p, 1.6 MB |
Clinical Profiles and Patterns of Kidney Disease Progression in C3 Glomerulopathy
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Caravaca-Fontan, Fernando (Universidad Complutense de Madrid) ;
Cavero Escribano, Teresa (Hospital 12 de Octubre (Madrid)) ;
Díaz Encarnación, Montserrat Mercedes (Fundació Puigvert) ;
Cabello, Virginia (Hospital Universitario Virgen del Rocío (Sevilla, Andalusia)) ;
Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Quintana, Luis F (Hospital Clínic i Provincial de Barcelona) ;
Marco Rusiñol, Helena (Fundació Puigvert) ;
Barros, Xoana (Hospital Universitari de Girona Doctor Josep Trueta) ;
Ramos Terrades, Natalia (Hospital Universitari Vall d'Hebron) ;
Rodríguez-Mendiola, Nuria (Hospital Universitario Ramón y Cajal (Madrid)) ;
Cruz, Sonia (Hospital Universitario Juan Ramón Jiménez) ;
Fernández-Juárez, Gema (Hospital Universitario La Paz (Madrid)) ;
Rodríguez, Adela (Hospital Universitario Virgen del Rocío (Sevilla, Andalusia)) ;
Pérez de José, Ana (Hospital General Universitario Gregorio Marañón) ;
Rabasco, Cristina (Hospital Universitario Reina Sofía (Córdoba, Espanya)) ;
Rodado, Raquel (Hospital Universitario Virgen de la Arrixaca (Múrcia)) ;
Fernández, Loreto (Complejo Hospitalario de Navarra) ;
Pérez-Gómez, Vanessa (Hospital Universitario Fundación Jiménez Díaz) ;
Ávila, Ana (Hospital Universitari Doctor Peset (València)) ;
Bravo, Luis (Complejo Hospitalario Universitario de A Coruña) ;
Espinosa, Natalia (Hospital Universitari Son Espases (Palma de Mallorca, Balears)) ;
Allende, Natalia (Hospital Universitari Son Espases (Palma de Mallorca, Balears)) ;
Sanchez de la Nieta, Maria Dolores (Hospital General Universitario de Ciudad Real) ;
Rodríguez García, Eva (Hospital del Mar (Barcelona, Catalunya)) ;
Rivas, Begoña (Hospital Universitario La Paz (Madrid)) ;
Melgosa, Marta (Hospital Universitario La Paz (Madrid)) ;
Huerta, Ana (Hospital Universitario Puerta de Hierro Majadahonda (Madrid)) ;
Miquel, Rosa (Hospital Universitario Canarias) ;
Mon, Carmen (Hospital Universitario Severo Ochoa) ;
Fraga Rodríguez, Gloria María (Hospital de la Santa Creu i Sant Pau (Barcelona, Catalunya)) ;
De Lorenzo, Alberto (Hospital Universitario de Getafe (Madrid)) ;
Draibe, Juliana (Hospital Universitari de Bellvitge) ;
González, Fayna (Hospital Universitario de Gran Canaria Dr. Negrín) ;
Shabaka, Amir (Hospital Universitario Clínico San Carlos (Madrid)) ;
López-Rubio, Maria Esperanza (Complejo Hospitalario Universitario de Albacete) ;
Fenollosa, María Ángeles (Consorci Hospitalari Provincial de Castelló) ;
Martín-Penagos, Luis (Hospital Universitario Marqués de Valdecilla (Santander, Cantabria)) ;
Da Silva, Iara (Institut Germans Trias i Pujol. Hospital Universitari Germans Trias i Pujol) ;
Titos, Juana Alonso (Hospital Regional Universitario Carlos Haya (Málaga)) ;
Rodríguez de Córdoba, Santiago (Centro de Investigación Biomédica en Red de Enfermedades Raras) ;
Goicoechea de Jorge, Elena (Universidad Complutense de Madrid) ;
Praga, Manuel (Hospital 12 de Octubre (Madrid)) ;
Universitat Autònoma de Barcelona
C3 glomerulopathy is a rare kidney disease, which makes it difficult to collect large cohorts of patients to better understand its variability. The aims of this study were to describe the clinical profiles and patterns of progression of kidney disease. [...]
2023 - 10.34067/KID.0000000000000115
Kidney360, Vol. 4 (march 2023) , p. 659-672
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13 p, 1.9 MB |
Multi-population genome-wide association study implicates immune and non-immune factors in pediatric steroid-sensitive nephrotic syndrome
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Barry, Alexandra (Broad Institute of MIT and Harvard) ;
McNulty, Michelle T. (Broad Institute of MIT and Harvard) ;
Jia, Xiaoyuan (The University of Tokyo) ;
Gupta, Yask (Columbia University College of Physicians and Surgeons) ;
Debiec, Hanna (Institut National de la Santé et de la Recherde Médicale) ;
Luo, Yang (Broad Institute of MIT and Harvard) ;
Nagano, China (Kobe University Graduate School of Medicine) ;
Horinouchi, Tomoko (Kobe University Graduate School of Medicine) ;
Jung, Seulgi (University of Ulsan College of Medicine) ;
Colucci, Manuela (Istituto di Ricovero e Cura a Carattere Scientifico Ospedale Pediatrico Bambino Gesù) ;
Ahram, Dina F. (Columbia University College of Physicians and Surgeons) ;
Mitrotti, Adele (University of Bari Aldo Moro) ;
Sinha, Aditi (AIIMS) ;
Teeninga, Nynke (Radboud University Medical Center) ;
Jin, Gina (Columbia University College of Physicians and Surgeons) ;
Shril, Shirlee (Harvard Medical School) ;
Caridi, Gianluca (IRCCS Instituto Giannina Gaslini) ;
Bodria, Monica (IRCCS Instituto Giannina Gaslini) ;
Lim, Tze Y. (Columbia University College of Physicians and Surgeons) ;
Westland, Rik (Amsterdam UMC. University Medical Center) ;
Zanoni, Francesca (University of Pennsylvania) ;
Marasa, Maddalena (Columbia University College of Physicians and Surgeons) ;
Turudic, Daniel (University of Zagreb Medical School) ;
Giordano, Mario (Bari Polyclinic Giovanni XXIII Children's Hospital) ;
Gesualdo, Loreto (University of Bari Aldo Moro) ;
Magistroni, Riccardo (University of Modena and Reggio Emilia) ;
Pisani, Isabella (Università di Parma) ;
Fiaccadori, Enrico (Università di Parma) ;
Reiterova, Jana (Charles University) ;
Maringhini, Silvio (ISMETT) ;
Morello, William (Fondazione IRCCS Ca' Granda-Ospedale Maggiore Policlinico) ;
Montini, Giovanni (University of Milan) ;
Weng, Patricia L. (UCLA Medical Center and UCLA Medical Center-Santa Monica) ;
Scolari, Francesco (University of Brescia and ASST Spedali Civili of Brescia) ;
Saraga, Marijan (University of Split) ;
Tasic, Velibor (University Children's Hospital Macedonia) ;
Santoro, Domenica (University of Messina) ;
van Wijk, Joanna A. E. (Amsterdam UMC. University Medical Center) ;
Milošević, Danko (Croatian Academy of Medical Sciences) ;
Kawai, Yosuke (The University of Tokyo) ;
Kiryluk, Krzysztof (Columbia University College of Physicians and Surgeons) ;
Pollak, Martin R. (Columbia University Irving Medical Center New York-Presbyterian Morgan Stanley Children's Hospital in New York) ;
Gharavi, Ali (Columbia University College of Physicians and Surgeons) ;
Lin, Fangmin (Columbia University Irving Medical Center New York-Presbyterian Morgan Stanley Children's Hospital in New York) ;
Simœs e Silva, Ana Cristina (Federal University of Minas Gerais) ;
Loos, Ruth J. F. (Icahn School of Medicine at Mount Sinai) ;
Kenny, Eimear E. (Icahn School of Medicine at Mount Sinai) ;
Schreuder, Michiel F. (Radboud University Medical Center) ;
Zurowska, Aleksandra (Medical University Gdansk.) ;
Dossier, Claire (Hôpital Robert-Debré) ;
Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Drozynska-Duklas, Magdalena (Medical University Gdansk) ;
Hogan, Julien (Hôpital Robert-Debré) ;
Jankauskiene, Augustina (Vilnius University) ;
Hildebrandt, Friedhelm (Harvard Medical School) ;
Prikhodina, Larisa (Pirogov Russian National Research Medical University) ;
Song, Kyuyoung (University of Ulsan College of Medicine) ;
Bagga, Arvind (AIIMS) ;
Cheong, Hae (Hallym University Sacred Heart Hospital) ;
Ghiggeri, Gian Marco (IRCCS Instituto Giannina Gaslini) ;
Vachvanichsanong, Prayong (Prince of Songkla University) ;
Nozu, Kandai (Kobe University Graduate School of Medicine) ;
Lee, Dongwon (Harvard Medical School) ;
Vivarelli, Marina (Istituto di Ricovero e Cura a Carattere Scientifico Ospedale Pediatrico Bambino Gesù) ;
Raychaudhuri, Soumya (University of Manchester) ;
Tokunaga, Katsushi (The University of Tokyo) ;
Sanna-Cherchi, Simone (Columbia University College of Physicians and Surgeons) ;
Ronco, Pierre (Centre Hospitalier du Mans) ;
Iijima, Kazumoto (Kobe University Graduate School of Medicine) ;
Sampson, Matthew G. (Brigham and Women's Hospital (Boston, Estats Units d'Amèrica)) ;
Universitat Autònoma de Barcelona
Pediatric steroid-sensitive nephrotic syndrome (pSSNS) is the most common childhood glomerular disease. Previous genome-wide association studies (GWAS) identified a risk locus in the HLA Class II region and three additional independent risk loci. [...]
2023 - 10.1038/s41467-023-37985-w
Nature communications, Vol. 14 (april 2023)
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11 p, 1.8 MB |
Development and validation of a nomogram to predict kidney survival at baseline in patients with C3 glomerulopathy
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Caravaca-Fontan, Fernando (Instituto de Investigación Sanitaria Hospital 12 de Octubre (i+12)) ;
Rivero, Marta (Hospital Universitario 12 de Octubre (Madrid)) ;
Cavero Escribano, Teresa (Hospital Universitario 12 de Octubre (Madrid)) ;
Díaz Encarnación, Montserrat Mercedes (Institut d'Investigació Biomèdica Sant Pau) ;
Cabello, Virginia (Hospital Universitario Virgen del Rocío (Sevilla, Andalusia)) ;
Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Quintana, Luis F (Hospital Clínic i Provincial de Barcelona) ;
Marco, Helena (Institut Germans Trias i Pujol. Hospital Universitari Germans Trias i Pujol) ;
Barros, Xoana (Hospital Universitari de Girona Doctor Josep Trueta) ;
Ramos Terrades, Natalia (Hospital Universitari Vall d'Hebron) ;
Rodríguez-Mendiola, Nuria (Hospital Universitario Ramón y Cajal (Madrid)) ;
Cruz, Sonia (Hospital Juan Ramón Jiménez (Huelva)) ;
Fernández-Juárez, Gema (Hospital Universitario Fundación Alcorcón) ;
Rodríguez Barba, Adela (Hospital Universitario Virgen del Rocío (Sevilla, Andalusia)) ;
Pérez de José, Ana (Hospital General Universitario Gregorio Marañón) ;
Rabasco, Cristina (Department of Nephrology. Hospital Universitario Reina Sofía (Córdoba, Espanya)) ;
Rodado, Raquel (Hospital Universitario Virgen de la Arrixaca (Múrcia)) ;
Fernández, Loreto (Department of Nephrology. Complejo Hospitalario de Navarra) ;
Pérez-Gómez, Maria Vanessa (Hospital Universitario Fundación Jiménez Díaz) ;
Ávila, Ana (Hospital Universitari Doctor Peset (València)) ;
Bravo, Luis (Complejo Hospitalario Universitario de A Coruña) ;
Espinosa, Natalia (Hospital Universitari Son Espases (Palma de Mallorca, Balears)) ;
Allende, Natalia (Hospital Universitari Son Espases (Palma de Mallorca, Balears)) ;
Sanchez De La Nieta, María Dolores (Hospital General Universitario de Ciudad Real) ;
Rodríguez, Eva (Hospital del Mar (Barcelona, Catalunya)) ;
Olea, Teresa (Hospital Universitario La Paz (Madrid)) ;
Melgosa, Marta (Hospital Universitario La Paz (Madrid)) ;
Huerta, Ana (Hospital Universitario Puerta de Hierro Majadahonda (Madrid)) ;
Miquel, Rosa (Hospital Universitario Canarias) ;
Mon, Carmen (Hospital Universitario Severo Ochoa Leganés) ;
Fraga Rodríguez, Gloria María (Institut d'Investigació Biomèdica Sant Pau) ;
De Lorenzo, Alberto (Hospital Universitario de Getafe (Madrid)) ;
Draibe, Juliana (Hospital Universitari de Bellvitge) ;
González, Fayna (Hospital Universitario de Gran Canaria Dr. Negrín) ;
Shabaka, Amir (Hospital Universitario Clínico San Carlos (Madrid)) ;
López-Rubio, María Esperanza (Complejo Hospitalario Universitario de Albacete) ;
Fenollosa, María Ángeles (Consorci Hospitalari Provincial de Castelló) ;
Martín-Penagos, Luis (Hospital Universitario Marqués de Valdecilla (Santander, Cantabria)) ;
Da Silva, Iara (Institut Germans Trias i Pujol. Hospital Universitari Germans Trias i Pujol) ;
Alonso Titos, Juana (Hospital Regional Universitario Carlos Haya (Málaga)) ;
Rodríguez De Córdoba, Santiago (Centro de Investigación Biomédica en Red de Enfermedades Raras) ;
Goicoechea De Jorge, Elena (Instituto de Investigación Sanitaria Hospital 12 de Octubre (i+12)) ;
Praga, Manuel (Hospital Universitario 12 de Octubre (Madrid)) ;
Universitat Autònoma de Barcelona
Background: C3 glomerulopathy is a rare and heterogeneous complement-driven disease. It is often challenging to accurately predict in clinical practice the individual kidney prognosis at baseline. We herein sought to develop and validate a prognostic nomogram to predict long-Term kidney survival. [...]
2022 - 10.1093/ckj/sfac108
Clinical Kidney Journal, Vol. 15 Núm. 9 (january 2022) , p. 1737-1746
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8 p, 418.9 KB |
Stress and coping strategies of families of pediatric solid organ transplant recipients in times of pandemic
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Forner-Puntonet, Mireia (Universitat Autònoma de Barcelona. Departament de Psiquiatria i de Medicina Legal) ;
Gisbert-Gustemps, Laura (Universitat Autònoma de Barcelona. Departament de Psiquiatria i de Medicina Legal) ;
Castell-Panisello, Eudald (Hospital Universitari Vall d'Hebron) ;
Larrarte, Mauricio (Hospital Universitari Vall d'Hebron) ;
Quintero, Jesús (Hospital Universitari Vall d'Hebron) ;
Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Gran, Ferran (Hospital Universitari Vall d'Hebron) ;
Iglesias-Serrano, Ignacio (Hospital Universitari Vall d'Hebron) ;
Garcia-Morán, Annabella (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Español-Martín, Gemma (Universitat Autònoma de Barcelona. Departament de Psiquiatria i de Medicina Legal) ;
Ibáñez, Pol (Hospital Universitari Vall d'Hebron. Institut de Recerca) ;
Ramos-Quiroga, Josep Antoni (Centro de Investigación Biomédica en Red de Salud Mental)
Pediatric solid organ transplantation (SOT) is a chronic condition that impacts the whole family system. The objective of this study is to evaluate psychopathology, family stress, and coping strategies in families of SOT recipients compared to families of healthy children and adolescents. [...]
2023 - 10.3389/fpsyg.2023.1067477
Frontiers in psychology, Vol. 14 (january 2023)
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10.
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13 p, 1.8 MB |
The long-acting C5 inhibitor, ravulizumab, is effective and safe in pediatric patients with atypical hemolytic uremic syndrome naïve to complement inhibitor treatment
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Ariceta Iraola, Gema (Hospital Universitari Vall d'Hebron) ;
Dixon, B.P. (Renal Section. Department of Pediatrics. University of Colorado School of Medicine) ;
Kim, S.H. (Department of Pediatrics. Pusan National University Children's Hospital) ;
Kapur, G. (Faculty of Pediatric Sciences. Central Michigan University. Mount Pleasant) ;
Mauch, T. (Department of Nephrology and Hypertension. Division of Pediatrics. University of Utah) ;
Ortiz, S. (Clinical and Non-Clinical Pharmacology. Alexion Pharmaceuticals Inc.) ;
Vallee, M. (Biostatistics. Alexion Pharmaceuticals Inc.) ;
Denker, A.E. (Clinical Development. Alexion Pharmaceuticals Inc.) ;
Kang, H.G. (Division of Pediatric Nephrology. Department of Pediatrics. Seoul National University College of Medicine) ;
Greenbaum, L.A. (Division of Pediatric Nephrology. Emory University School of Medicine and Children's Healthcare of Atlanta) ;
Lovell, H. ;
Muff-Luett, M. ;
Malone, K. ;
Adeagbo, O. ;
Wilkerson, A. ;
Fraga Rodríguez, Gloria María (Institut d'Investigació Biomèdica Sant Pau) ;
Sarri, S. ;
Cheong, H.I. ;
Ahn, Y.H. ;
Han, K.H.
Ravulizumab, a long-acting complement C5 inhibitor engineered from eculizumab, allows extending maintenance dosing from every 2-3 weeks to every 4-8 weeks depending on bodyweight. Here, we evaluated the efficacy and safety of ravulizumab in complement inhibitor-naïve children (under 18 years) with atypical hemolytic uremic syndrome. [...]
2021 - 10.1016/j.kint.2020.10.046
Kidney International, Vol. 100 Núm. 1 (july 2021) , p. 225-237
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