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16 p, 3.7 MB Vulnerability of progeroid smooth muscle cells to biomechanical forces is mediated by MMP13 / Pitrez, Patricia R. (University of Coimbra) ; Estronca, Luís (University of Coimbra) ; Monteiro, Luís Miguel (University of Coimbra) ; Colell, Guillem (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Vazão, Helena (University of Coimbra) ; Santinha, Deolinda (University of Coimbra) ; Harhouri, Karim (Aix Marseille Univ) ; Thornton, Daniel (University of Liverpool) ; Navarro, Claire (Progelife (França)) ; Egesipe, Anne-Laure (Institute for Stem Cell Therapy and Exploration of Monogenic Diseases) ; Carvalho, Tânia (Universidade de Lisboa) ; Dos Santos, Rodrigo L. (Cambridge Science Park) ; Lévy, Nicolas (La Timone Children's Hospital) ; Smith, James C. (Francis Crick Institute) ; de Magalhaes, Joao Pedro (University of Liverpool. Integrative Genomics of Ageing Group, Institute of Ageing and Chronic Disease) ; Ori, Alessandro (Leibniz Institute on Aging) ; Bernardo, Andreia (Francis Crick Institute) ; De Sandre-Giovannoli, Annachiara (CRB Assistance Publique des Hôpitaux de Marseille) ; Nissan, Xavier (Institute for Stem Cell Therapy and Exploration of Monogenic Diseases (França)) ; Rosell Novel, Anna (Hospital Universitari Vall d'Hebron. Institut de Recerca) ; Ferreira, Lino (University of Coimbra) ; Universitat Autònoma de Barcelona
Hutchinson-Gilford Progeria Syndrome (HGPS) is a premature aging disease in children that leads to early death. Smooth muscle cells (SMCs) are the most affected cells in HGPS individuals, although the reason for such vulnerability remains poorly understood. [...]
2020 - 10.1038/s41467-020-17901-2
Nature communications, Vol. 11 (august 2020)  

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1 Navarro, Cristóbal A.
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