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10 p, 876.7 KB Measuring cognitive impairment and monitoring cognitive decline in Huntington's disease : a comparison of assessment instruments / Horta, Andrea (Universitat Autònoma de Barcelona. Departament de Medicina) ; Martinez-Horta, Saul (Universitat Autònoma de Barcelona. Departament de Medicina) ; Pérez-Pérez, Jesús (Universitat Autònoma de Barcelona. Departament de Medicina) ; Puig-Davi, Arnau (Institut d'Investigació Biomèdica Sant Pau) ; de Lucia, Natascia (University of Naples "Federico II", Naples, Italy) ; de Michele, Giuseppe (University of Naples "Federico II", Naples, Italy) ; Salvatore, Elena (University of Naples "Federico II", Naples, Italy) ; Kehrer, Stefanie (Charité-Universitätsmedizin, Berlin, Germany) ; Priller, Josef (Charité-Universitätsmedizin, Berlin, Germany) ; Migliore, Simone (Fondazione IRCCS Casa Sollievo Della Sofferenza Research Hospital, San Giovanni Rotondo, Italy) ; Squitieri, Ferdinando (Fondazione IRCCS Casa Sollievo Della Sofferenza Research Hospital, San Giovanni Rotondo, Italy) ; Castaldo, Ana (Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy) ; Mariotti, Caterina (Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy) ; Mañanes, Verónica (Hospital Universitario Ramon Y Cajal) ; Lopez-Sendon, José Luís (Hospital Universitario Ramon Y Cajal) ; Rodriguez, Noelia (Fundación Jimenez Diaz) ; Martinez-Descals, Asunción (Fundación Jimenez Diaz) ; Júlio, Filipa (Coimbra University Hospital) ; Januário, Cristina (Coimbra University Hospital) ; Delussi, marianna (European Huntington's Disease Network (EHDN), Ulm, Germany) ; de Tommaso, Marina (European Huntington's Disease Network (EHDN), Ulm, Germany) ; Noguera, Sandra (Hospital Mare de Deu de La Mercè) ; Ruiz-Idiago, Jesús (Hospital Mare de Deu de La Mercè) ; Sitek, Emilia J. (St. Adalbert Hospital, Copernicus, Gdańsk, Poland) ; Wallner, Renata (Medical University of Wroclaw, Wroclaw, Poland) ; Nuzzi, Angela (European Huntington's Disease Network (EHDN), Ulm, Germany) ; Pagonabarraga Mora, Javier (Universitat Autònoma de Barcelona. Departament de Medicina) ; Kulisevsky, Jaime (Universitat Autònoma de Barcelona. Departament de Medicina)
Background: Progressive cognitive decline is an inevitable feature of Huntington's disease (HD) but specific criteria and instruments are still insufficiently developed to reliably classify patients into categories of cognitive severity and to monitor the progression of cognitive impairment. [...]
2023 - 10.1007/s00415-023-11804-0
Journal of Neurology, Vol. 270, Num. 11 (november 2023) , p. 5408-5417  

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