Latest additions:
2024-05-21
08:04
Cognitive phenotype and neurodegeneration associated with Tau in Huntington's disease / Martinez-Horta, S. (European Huntington's Disease Network (EHDN)) ; Perez-Perez, J. (European Huntington's Disease Network (EHDN)) ; Perez-Gonzalez, R. (Instituto de Investigación Sanitaria y Biomédica de Alicante (ISABIAL) and Instituto de Neurociencias UMH-CSIC) ; Sampedro, F. (Neuroradiology unit. Radiology Department. Hospital de la Santa Creu i Sant Pau) ; Horta-Barba, A. (European Huntington's Disease Network (EHDN)) ; Campolongo, A. (Universitat Autònoma de Barcelona. Departament de Medicina) ; Rivas-Asensio, E. (Centro de Investigación Biomédica en Red-Enfermedades Neurodegenerativas (CIBERNED)) ; Puig-Davi, A. (European Huntington's Disease Network (EHDN)) ; Pagonabarraga, J. (European Huntington's Disease Network (EHDN)) ; Kulisevsky, J. (European Huntington's Disease Network (EHDN))
Objective: The clinical phenotype of Huntington's disease (HD) can be very heterogeneous between patients, even when they share equivalent CAG repeat length, age, or disease burden. This heterogeneity is especially evident in terms of the cognitive profile and related brain changes. [...]
2024 - 10.1002/acn3.52031
Annals of Clinical and Translational Neurology, Vol. 11 Núm. 5 (may 2024) , p. 1160-1171  
2024-05-21
08:03
Adapting prescribing criteria for amyloid-targeted antibodies for adults with Down syndrome / Hillerstrom, H. (LuMind IDSC Foundation) ; Fisher, R. (LuMind IDSC Foundation) ; Janicki, M.P. (National Task Group on Intellectual Disabilities and Dementia Practices) ; Chicoine, B. (Advocate Health. Advocate Medical Group Adult Down Syndrome Center. Advocate Lutheran General Hospital Family Medicine Residency) ; Christian, B.T. (Waisman Center IDDRC. University of Wisconsin) ; Esbensen, A. (Division of Developmental and Behavioral Pediatrics. Cincinnati Children's Hospital Medical Center. University of Cincinnati College of Medicine. Cincinnati Children's Hospital) ; Esralew, L. (California Department of Developmental Services) ; Fortea, J. (Institut d'Investigació Biomèdica Sant Pau) ; Hartley, S. (Waisman Center IDDRC. University of Wisconsin) ; Hassenstab, J. (Departments of Neurology and Psychological & Brain Sciences. Knight Alzheimer Disease Research Center. Washington University) ; Keller, S.M. (Neurology Associates of South Jersey) ; Krinsky-McHale, S. (Department of Psychology. New York State Institute for Basic Research in Developmental Disabilities) ; Lai, F. (MGH Neurology Research. Mass General Brigham Hospital. Massachusetts General Hospital) ; Levin, J. (Department of Neurology. Sahgrenska University Hospital) ; McCarron, M. (Trinity Centre for Ageing and Intellectual Disability. Trinity College. University of Dublin) ; McDade, E. (Departments of Neurology and Psychological & Brain Sciences. Knight Alzheimer Disease Research Center. Washington University) ; Rebillat, A.S. (Outpatient Department. Institut Jerome Lejeune) ; Rosas, H.D. (Department of Radiology. Athinoula Martinos Center. Massachusetts General Hospital. Harvard Medical School) ; Silverman, W. (Department of Pediatrics. University of California Irvine) ; Strydom, A. (Institute of Psychiatry. Psychology and Neuroscience. Kings College) ; Zaman, S.H. (Department of Psychiatry. Cambridge Intellectual and Developmental Disabilities Research Group. Cambridge University) ; Zetterberg, H. (Munich Cluster for Systems Neurology (SyNergy))
Prior authorization criteria for Federal Drug Administration (FDA) approved immunotherapeutics, among the class of anti-amyloid monoclonal antibodies (mAbs), established by state drug formulary committees, are tailored for adults with late-onset Alzheimer's disease. [...]
2024 - 10.1002/alz.13778
Alzheimer's & Dementia, Vol. 20 Núm. 5 (may 2024) , p. 3649-3656  
2024-05-21
07:58
Evolution of invasive pneumococcal disease by serotype 3 in adults : a Spanish three-decade retrospective study / Calvo-Silveria, S. (Research Network for Respiratory Diseases (CIBERES). ISCIII) ; González-Díaz, A. (Research Network for Respiratory Diseases (CIBERES). ISCIII) ; Grau, I. (Infectious Diseases Department. Hospital Universitari de Bellvitge - IDIBELL. L'Hospitalet de Llobregat) ; Marimón, J.M. (Biogipuzkoa. Infectious Diseases Area. Respiratory Infection and Antimicrobial Resistance Group. Microbiology Department. Hospital Donostia. Osakidetza Basque Health Service) ; Cercenado, E. (Clinical Microbiology and Infectious Disease Department. Hospital General Universitario Gregorio Marañón) ; Quesada, M.D. (Microbiology Department. Clinical Laboratory North Metropolitan Area. Hospital Universitari Germans Trias i Pujol. UAB) ; Casabella, A. (Institut d'Investigació i Innovació Parc Taulí (I3PT). Universitat Autònoma de Barcelona) ; Larrosa, N. (Research Network for Infectious Diseases (CIBERINFEC). ISCIII) ; Yuste, J. (Spanish Pneumococcal Reference Laboratory. National Centre for Microbiology. Instituto de Salud Carlos III) ; Berbel, D. (Research Network for Respiratory Diseases (CIBERES). ISCIII) ; Alonso, M. (Biogipuzkoa. Infectious Diseases Area. Respiratory Infection and Antimicrobial Resistance Group. Microbiology Department. Hospital Donostia. Osakidetza Basque Health Service) ; Tubau, F. (Research Network for Respiratory Diseases (CIBERES). ISCIII) ; Belman, S. (Earth Sciences Department. Barcelona Supercomputing Center - Centro Nacional de Supercomputación) ; Cadenas-Jiménez, I. (Research Network for Respiratory Diseases (CIBERES). ISCIII) ; Martín-Galiano, A.J. (Core Scientific and Technical Units. Instituto de Salud Carlos III) ; Domínguez, M.Á. (Department of Pathology and Experimental Therapeutics. University of Barcelona) ; Martí, S. (Department of Medicine. School of Medicine and Health Sciences. University of Barcelona) ; Liñares, J. (Microbiology Department. Hospital Universitari de Bellvitge - IDIBELL. L'Hospitalet de Llobregat) ; Pallarés, R. (Department of Clinical Sciences. University of Barcelona) ; Càmara, J. (Research Network for Respiratory Diseases (CIBERES). ISCIII) ; Ardanuy, Carmen (Department of Pathology and Experimental Therapeutics. University of Barcelona)
Background: Invasive pneumococcal disease due to serotype 3 (S3-IPD) is associated with high mortality rates and long-term adverse effects. The introduction of the 13-valent pneumococcal conjugate vaccine (PCV13) into the Spanish paediatric immunisation programme has not led to a decrease in the adult S3-IPD. [...]
2024 - 10.1016/j.lanepe.2024.100913
The Lancet Regional Health - Europe, Vol. 41 (june 2024) , p. 100913  
2024-05-18
21:53
Exploring new paths towards game accessibility / Mangiron, Carme
Brill 2012
Audiovisual translation and media accessibility at the crossroads, 2012, p. 43-59
   
2024-05-18
12:32
26 p, 240.5 KB Subtitling in game localisation: a descriptive study / Mangiron, Carme
2013 - https://doi.org/10.1080/0907676X.2012.722653
Perspectives Studies in Translation Theory and Practice, Vol. 21 Núm. 1 (2013)  
2024-05-18
11:59
14 p, 2.1 MB Learning to collaborate within transdisciplinarity : internal barriers and strengths of an art-science encounter / Gallois, Sandrine (Institute of Environmental Science and Technology (ICTA-UAB). Laboratori d'Anàlisi de Sistemes Socio-Ecològics en la Globalització (LASEG). Internet Interdisciplinary Institute. Universitat Oberta de Catalunya (UOC)) ; Heras López, María (Faculty of Arts and Humanities. Institute of Environmental Science and Technology (ICTA-UAB). Internet Interdisciplinary Institute. Universitat Oberta de Catalunya (UOC)) ; Sella, Carlo (Independent Artist) ; Satorras, Mar (Universitat Oberta de Catalunya (UOC). Universitat Autònoma de Barcelona (UAB)) ; Ribera-Fumaz, Ramon (Universitat Oberta de Catalunya) ; Ruiz Mallén, Isabel (Universitat Autònoma de Barcelona. Departament de Pediatria, Obstetrícia i Ginecologia i Medicina Preventiva i Salut Pública)
Despite the recognized importance of transdisciplinarity, including art-science collaborations, for tackling the complex challenges of the Anthropocene, little is known about the internal mechanisms of such alliances. [...]
Despite the recognized importance of transdisciplinarity, including art-science collaborations, for tackling the complex challenges of the Anthropocene, little is known about the internal mechanisms of such alliances. [...]

Springer Japan, 2024 - 10.1007/s11625-024-01495-5
Sustainability Science  
2024-05-18
11:59
21 p, 3.8 MB A critical trade-off between nitrogen quota and growth allows Coccolithus braarudii life cycle phases to exploit varying environment / de Vries, Joost (University of Bristol. Marine Biological Association) ; Monteiro, Fanny (University of Bristol) ; Langer, Gerald (Institute of Environmental Science and Technology (ICTA-UAB). Marine and Environmental Biogeosciences Research Group (MERS)) ; Brownlee, Colin (Marine Biological Association) ; Wheeler, Glen (Universitat Autònoma de Barcelona) ; Universitat Autònoma de Barcelona. SGR - Grup de Recerca Marines and Environmental Biogeosciences Research Group - MERS
Coccolithophores have a distinct haplo-diplontic life cycle, which allows them to grow and divide into two different life cycle phases (haploid and diploid). These life cycle phases vary significantly in inorganic carbon content and morphology and inhabit distinct niches, with haploids generally preferring low-nitrogen and high-temperature and high-light environments in situ. [...]
Coccolithophores have a distinct haplo-diplontic life cycle, which allows them to grow and divide into two different life cycle phases (haploid and diploid). These life cycle phases vary significantly in inorganic carbon content and morphology and inhabit distinct niches, with haploids generally preferring low-nitrogen and high-temperature and high-light environments in situ. [...]

2024 - 10.5194/bg-21-1707-2024
Biogeosciences, Vol. 21 Núm. 7 (2024) , p. 1707-1727  
2024-05-18
11:59
3 p, 679.0 KB Correction to : Coccolith-calcite Sr/Ca as a proxy for transient export production related to Saharan dust deposition in the tropical North Atlantic (Scientific Reports, (2024), 14, 1, (4295), 10.1038/s41598-024-54001-3) / Guerreiro, C. V. (University of Lisbon. IDL. FCUL) ; Ziveri, Patrizia (Institute of Environmental Science and Technology (ICTA-UAB). Marine and Environmental Biogeosciences Research Group (MERS). Catalan Institution for Research and Advanced Studies (ICREA)) ; Cavaleiro, C. (IPMA - Portuguese Institute for Sea and Atmosphere) ; Stuut, J. B.W. (Universitat Autònoma de Barcelona. SGR - Grup de Recerca Marines and Environmental Biogeosciences Research Group - MERS)
Correction to: Scientific Reportshttps://doi. org/10. 1038/s41598-024-54001-3, published online 21 February 2024 The original version of this Article contained a repeated error, where all instances of the unit 'µm' were incorrectly given as 'mm'. [...]
Correction to: Scientific Reportshttps://doi. org/10. 1038/s41598-024-54001-3, published online 21 February 2024 The original version of this Article contained a repeated error, where all instances of the unit 'µm' were incorrectly given as 'mm'. [...]

2024 - 10.1038/s41598-024-56736-5
Scientific reports, Vol. 14 Núm. 1 (2024)  
2024-05-18
11:59
36 p, 498.0 KB The Samurai Bond : credit Supply and Economic Growth in Pre-War Japan / Basco, Sergi (Department of Applied Economics) ; Tang, John (Universitat Autònoma de Barcelona. Departament d'Economia Aplicada)
While credit supply growth is associated with exacerbating financial crises, its impact on long-run development is unclear. Using bond payments to samurai in nineteenth century Japan as a quasi-natural experiment and exploiting regional variation, we find that bond payments are associated with persistent redistributive effects between regions and sectors. [...]
2018 - 10.7916/D8BK2VWR  
2024-05-18
04:31
15 p, 2.4 MB Spanish registry of hemoglobinopathies and rare anemias (REHem-AR) : demographics, complications, and management of patients with β-thalassemia / Bardón-Cancho, Eduardo J. (Facultad de Medicina, Universidad Complutense de Madrid. Sección de Hematología y Oncología Pediátricas. Servicio de Pediatría. Hospital General Universitario Gregorio Marañón. Instituto de Investigación Sanitaria Gregorio Marañón. CSUR Eritropatología. ERN-EuroBloodNet. CIBERER) ; Marco-Sánchez, José Manuel (Facultad de Medicina, Universidad Complutense de Madrid. Sección de Hematología y Oncología Pediátricas. Servicio de Pediatría. Hospital General Universitario Gregorio Marañón. Instituto de Investigación Sanitaria Gregorio Marañón. CSUR Eritropatología. ERN-EuroBloodNet. CIBERER) ; Benéitez-Pastor, David (Universitat Autònoma de Barcelona. Grupo de Eritropatología SEHH. Grupo de Investigación Translacional en Anemias Minoritarias, Unidad de Eritropatología. Servicio de Hematología Clínica. Hospital Universitario Vall d'Hebron, Vall d'Hebron Institut de Recerca (VHIR) y Vall d'Hebron Institut d'Oncologia (VHIO), ERN-EuroBloodNet. CIBERER) ; Payán-Pernía, Salvador (Universidad de Sevilla. Servicio de Hematología. Hospital Universitario Virgen del Rocío, Instituto de Biomedicina de Sevilla (IBIS)-Consejo Superior de Investigaciones Científicas (CSIC)) ; Llobet, Anna Ruiz (Universitat de Barcelona. Servicio de Hematología Pediátrica. Hospital Sant Joan de Déu Barcelona, Institut de Recerca Pediàtrica Hospital San Joan de Déu de Barcelona (IRP-HSJD)) ; Berrueco, Rubén (Universitat de Barcelona. Servicio de Hematología Pediátrica. Hospital Sant Joan de Déu Barcelona, Institut de Recerca Pediàtrica Hospital San Joan de Déu de Barcelona (IRP-HSJD)) ; García-Morin, Marina (Facultad de Medicina, Universidad Complutense de Madrid. Sección de Hematología y Oncología Pediátricas. Servicio de Pediatría. Hospital General Universitario Gregorio Marañón. Instituto de Investigación Sanitaria Gregorio Marañón. CSUR Eritropatología. ERN-EuroBloodNet. CIBERER) ; Beléndez, Cristina (Facultad de Medicina, Universidad Complutense de Madrid. Sección de Hematología y Oncología Pediátricas. Servicio de Pediatría. Hospital General Universitario Gregorio Marañón. Instituto de Investigación Sanitaria Gregorio Marañón. CSUR Eritropatología. ERN-EuroBloodNet. CIBERER) ; Senent, Leonor (Hospital Universitario y Politécnico La Fe. Servicio de Hematología) ; Acosta, María José Ortega (Hospital Universitario Virgen de las Nieves. Servicio de Hematología Infantil) ; Pleguezuelos, Irene Peláez (Hospital Universitario Virgen de las Nieves. Servicio de Hematología Infantil) ; Velasco, Pablo (Hospital Universitario Vall d'Hebron. Servicio de Hematología Infantil) ; Collado, Anna (Hospital Universitario Vall d'Hebron. Servicio de Hematología Infantil) ; Moreno-Servet, Marta (Universidad Complutense de Madrid. Servicio de Hematología. Hospital General Universitario Gregorio Marañón. Instituto de Investigación Sanitaria Gregorio Marañón. CSUR Eritropatología. ERN-EuroBloodNet) ; Argilés, Bienvenida (Hospital Universitario y Politécnico La Fe. Servicio de Hematología Infantil) ; de Soto, Inmaculada Pérez (Universidad de Sevilla. Servicio de Hematología. Hospital Universitario Virgen del Rocío, Instituto de Biomedicina de Sevilla (IBIS)-Consejo Superior de Investigaciones Científicas (CSIC)) ; del Mar Bermúdez, María (Hospital Virgen de la Arrixaca. Servicio de Oncología Pediátrica) ; Salido Fiérrez, Eduardo J. (Hospital Virgen de la Arrixaca. Servicio de Hematología) ; Blanco, Adoración (Hospital Universitari Vall d'Hebron. Unitat de Genètica Molecular Hematològica. Servei d'Hematologia) ; Navarro, Pablo González (Hospital General Universitario Gregorio. Bioestadístico. Unidad de Investigación Materno Infantil. Fundación Familia Alonso (UDIMIFFA). Instituto de Investigación Sanitaria Gregorio Marañón (IiSGM)) ; Cela, Elena (Facultad de Medicina, Universidad Complutense de Madrid. Sección de Hematología y Oncología Pediátricas. Servicio de Pediatría. Hospital General Universitario Gregorio Marañón. Instituto de Investigación Sanitaria Gregorio Marañón. CSUR Eritropatología. ERN-EuroBloodNet. CIBERER)
The increase in the number of patients with hemoglobinopathies in Europe in recent decades highlights the need for more detailed epidemiological information in Spain. To fulfil this need, the Spanish Society of Pediatric Hematology and Oncology (SEHOP) sponsored the creation of a national registry of hemoglobinopathies known as REHem-AR (Spanish Registry of Hemoglobinopathies and Rare Anemias). [...]
2024 - 10.1007/s00277-024-05694-z
Annals of Hematology, Vol. 103 (march 2024) , p. 1525-1539