Results overview: Found 2 records in 0.01 seconds.
Articles, 2 records found
Articles 2 records found  
1.
12 p, 2.9 MB Muscle magnetic resonance imaging in myotonic dystrophy type 1 (DM1) : Refining muscle involvement and implications for clinical trials / Garibaldi, Matteo (Sant'Andrea Hospital) ; Nicoletti, Tommaso (Università Cattolica del Sacro Cuore) ; Bucci, Elisabetta (Sant'Andrea Hospital) ; Fionda, Laura (Sant'Andrea Hospital. Sapienza University of Rome) ; Leonardi, Luca (Sant'Andrea Hospital) ; Morino, Stefania (Sant'Andrea Hospital) ; Tufano, Laura (Sant'Andrea Hospital) ; Alfieri, Girolamo (Sant'Andrea Hospital) ; Lauletta, Antonio (Sant'Andrea Hospital) ; Merlonghi, Gioia (Sant'Andrea Hospital) ; Perna, Alessia (Università Cattolica del Sacro Cuore) ; Rossi, Salvatore (Università Cattolica del Sacro Cuore) ; Ricci, Enzo (Università Cattolica del Sacro Cuore) ; Alonso-Pérez, Jorge (Institut d'Investigació Biomèdica Sant Pau) ; Tartaglione, Tommaso (Istituto Dermopatico dell'Immacolata) ; Petrucci, Antonio (San Camillo Forlanini Hospital) ; Pennisi, Elena Maria (San Filippo Neri Hospital) ; Salvetti, Marco (IRCCS Istituto Neurologico Mediterraneo (INM) Neuromed) ; Cutter, Gary (University of Alabama at Birmingham) ; Diaz-Manera, Jordi (Institut d'Investigació Biomèdica Sant Pau) ; Silvestri, Gabriella (Università Cattolica del Sacro Cuore) ; Antonini, Giovanni (Sant'Andrea Hospital)
Only a few studies have reported muscle imaging data on small cohorts of patients with myotonic dystrophy type 1 (DM1). We aimed to investigate the muscle involvement in a large cohort of patients in order to refine the pattern of muscle involvement, to better understand the pathophysiological mechanisms of muscle weakness, and to identify potential imaging biomarkers for disease activity and severity. [...]
2021 - 10.1111/ene.15174
European Journal of Neurology, Vol. 29 (december 2021) , p. 843-854  
2.
15 p, 2.2 MB Muscle MRI in immune-mediated necrotizing myopathy (IMNM) : implications for clinical management and treatment strategies / Fionda, Laura (Università degli Studi di Roma La Sapienza) ; Lauletta, Antonio (Università degli Studi di Roma La Sapienza) ; Leonardi, Luca (Università degli Studi di Roma La Sapienza) ; Perez, Jorge Alonso (Hospital de la Santa Creu i Sant Pau (Barcelona, Catalunya)) ; Morino, Stefania (Università degli Studi di Roma La Sapienza) ; Merlonghi, Gioia (Università degli Studi di Roma La Sapienza) ; Alfieri, Girolamo (Università degli Studi di Roma La Sapienza) ; Costanzo, Rocco (Università degli Studi di Roma La Sapienza) ; Tufano, Laura (Università degli Studi di Roma La Sapienza) ; Vanoli, Fiammetta (IRCCS Istituto Neurologico Carlo Besta) ; Rossini, Elena (Università degli Studi di Roma La Sapienza) ; Vigo, Eduard Gallardo (Hospital de la Santa Creu i Sant Pau (Barcelona, Catalunya)) ; Tartaglione, Tommaso (Istituto Dermopatico dell'Immacolata (Itàlia)) ; Salvetti, Marco (Università degli Studi di Roma La Sapienza) ; Antonini, Giovanni (Università degli Studi di Roma La Sapienza) ; Diaz-Manera, Jordi (Centro de Investigación Biomédica en Red de Enfermedades Raras) ; Garibaldi, Matteo (Università degli Studi di Roma La Sapienza) ; Universitat Autònoma de Barcelona
Immune-mediated necrotizing myopathy (IMNM) is the most severe idiopathic inflammatory myopathy (IIM) and early aggressive poly-immunotherapy is often required to reduce long-term disability. The aim of this study is to investigate muscle MRI in IMNM as outcome measure for disease activity, severity, progression, response to treatment, and to better characterize the pattern of muscle involvement. [...]
2022 - 10.1007/s00415-022-11447-7
Journal of Neurology, Vol. 270 (november 2022) , p. 960-974  

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